The patient is a boy of five years old with asplenia, dextrocardia, right aortic arch, bilateral superior vena cavae, single atrium, common atrioventricular orifice, double outlet right ventricle and pulmonary stenosis. He underwent operations of right Blalock-Taussig shunt and right superior vena cava ligation when he was eight months old and at the age of three years old, bidirectional Glenn procedure and bivalvation of the common atrioventricular valve (CAVV) as he, then, suffered from severe regurgitation of the CAVV. The regurgitation improved from grade 3 to 1 and his recovery allowed the fenestrated Fontan operation at the age of four years and nine months. Bivalvation is an effective means for the mitigation of regurgitation of CAVV and paves the way for application of Fontan-type operation.