[Familial epilepsy seizure disclosing long QT syndrome]. 1996

T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
Service de Neurologie, Hôpital de l'Antiquaille, Lyon.

The Romano-Ward syndrome shows a congenital prolonged QT on the electrocardiogram. It is often revealed by syncopes, sudden death and, in rare cases, by an epileptic attack. We report the cases of two sisters presenting this syndrome. One of them presented an inaugural epileptic attack. The electrocardiogram returned to normal and the seizures disappeared after a treatment with beta-bloquants.

UI MeSH Term Description Entries
D008133 Long QT Syndrome A condition that is characterized by episodes of fainting (SYNCOPE) and varying degree of ventricular arrhythmia as indicated by the prolonged QT interval. The inherited forms are caused by mutation of genes encoding cardiac ion channel proteins. The two major forms are ROMANO-WARD SYNDROME and JERVELL-LANGE NIELSEN SYNDROME. Electrocardiogram QT Prolonged
D004827 Epilepsy A disorder characterized by recurrent episodes of paroxysmal brain dysfunction due to a sudden, disorderly, and excessive neuronal discharge. Epilepsy classification systems are generally based upon: (1) clinical features of the seizure episodes (e.g., motor seizure), (2) etiology (e.g., post-traumatic), (3) anatomic site of seizure origin (e.g., frontal lobe seizure), (4) tendency to spread to other structures in the brain, and (5) temporal patterns (e.g., nocturnal epilepsy). (From Adams et al., Principles of Neurology, 6th ed, p313) Aura,Awakening Epilepsy,Seizure Disorder,Epilepsy, Cryptogenic,Auras,Cryptogenic Epilepsies,Cryptogenic Epilepsy,Epilepsies,Epilepsies, Cryptogenic,Epilepsy, Awakening,Seizure Disorders
D005260 Female Females
D006801 Humans Members of the species Homo sapiens. Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D000328 Adult A person having attained full growth or maturity. Adults are of 19 through 44 years of age. For a person between 19 and 24 years of age, YOUNG ADULT is available. Adults

Related Publications

T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
June 1997, Revue neurologique,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
January 1986, Polski tygodnik lekarski (Warsaw, Poland : 1960),
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
June 2002, Saudi medical journal,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
September 1992, The American journal of emergency medicine,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
June 1985, IMJ. Illinois medical journal,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
July 2010, Fortschritte der Neurologie-Psychiatrie,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
February 2019, Practical neurology,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
January 2002, Revista de neurologia,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
February 1998, Nihon rinsho. Japanese journal of clinical medicine,
T Moreau, and S Thobois, and B Coppere, and J Ninet, and C Confavreux
December 2003, Indian pediatrics,
Copied contents to your clipboard!