Biomaterial Database

Maffucci's syndrome associated with spindle cell hemangioendothelioma. 1997

M Hisaoka, and T Aoki, and H Kouho, and H Chosa, and H Hashimoto

Department of Pathology and Oncology, School of Medicine, University of Occupational and Environmental Health, Yahatanishi-ku, Kitakyushu, Japan.

The case of a 49-year-old man with Maffucci's syndrome, who developed multiple spindle cell hemangioendotheliomas, is presented. The case provides support for recent reports suggesting an association between this peculiar vascular lesion and skeletal enchondromatosis.

UI	MeSH Term	Description	Entries
D008297	Male		Males
D008875	Middle Aged	An adult aged 45 - 64 years.	Middle Age
D004687	Enchondromatosis	Benign growths of cartilage in the metaphyses of several bones.	Enchondroma, Multiple,Enchondrosis, Multiple,Maffucci Syndrome,Ollier's Disease,Chondrodysplasia with Hemangioma,Chondroplasia Angiomatosis,Dyschondrodysplasia with Hemangiomas,Dyschondroplasia and Cavernous Hemangioma,Enchondromatosis with Hemangiomata,Enchondromatosis with Multiple Cavernous Hemangiomas,Enchondromatosis, Multiple,Hemangiomata with Dyschondroplasia,Hemangiomatosis Chondrodystrophica,Kast Syndrome,Multiple Angiomas and Endochondromas,Ollier Disease,Disease, Ollier,Disease, Ollier's,Enchondromas, Multiple,Enchondromatoses,Enchondroses, Multiple,Multiple Enchondroma,Multiple Enchondromas,Multiple Enchondroses,Multiple Enchondrosis,Olliers Disease,Syndrome, Maffucci
D006225	Hand	The distal part of the arm beyond the wrist in humans and primates, that includes the palm, fingers, and thumb.	Hands
D006390	Hemangioendothelioma	A neoplasm derived from blood vessels, characterized by numerous prominent endothelial cells that occur singly, in aggregates, and as the lining of congeries of vascular tubes or channels. Hemangioendotheliomas are relatively rare and are of intermediate malignancy (between benign hemangiomas and conventional angiosarcomas). They affect men and women about equally and rarely develop in childhood. (From Stedman, 25th ed; Holland et al., Cancer Medicine, 3d ed, p1866)	Endothelioma, Vascular,Hemangio-Endothelioma,Endotheliomas, Vascular,Hemangio Endothelioma,Hemangio-Endotheliomas,Hemangioendotheliomas,Vascular Endothelioma,Vascular Endotheliomas
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D015901	Angiography, Digital Subtraction	A method of delineating blood vessels by subtracting a tissue background image from an image of tissue plus intravascular contrast material that attenuates the X-ray photons. The background image is determined from a digitized image taken a few moments before injection of the contrast material. The resulting angiogram is a high-contrast image of the vessel. This subtraction technique allows extraction of a high-intensity signal from the superimposed background information. The image is thus the result of the differential absorption of X-rays by different tissues.	Digital Subtraction Angiography,Subtraction Angiography, Digital