Biomaterial Database

Correction of anomalous systemic venous drainage in heterotaxy syndrome. 1997

A X Palacios-Macedo, and C D Fraser

Congenital Heart Surgery Service, Texas Children's Hospital, Houston 77030-2399, USA.

A 3-month-old patient with heterotaxy syndrome, complex intracardiac malformations, and severe heart failure underwent surgical correction. Anatomy included an interrupted inferior vena cava with hemiazygous continuation to a persistent left superior vena cava draining to the left atrium. The presence of partial anomalous pulmonary venous drainage precluded an intraatrial baffle. Systemic venous reconstruction was achieved using the left atrial appendage along with an intracardiac repair of the other defects.

UI	MeSH Term	Description	Entries
D007223	Infant	A child between 1 and 23 months of age.	Infants
D006330	Heart Defects, Congenital	Developmental abnormalities involving structures of the heart. These defects are present at birth but may be discovered later in life.	Congenital Heart Disease,Heart Abnormalities,Abnormality, Heart,Congenital Heart Defect,Congenital Heart Defects,Defects, Congenital Heart,Heart Defect, Congenital,Heart, Malformation Of,Congenital Heart Diseases,Defect, Congenital Heart,Disease, Congenital Heart,Heart Abnormality,Heart Disease, Congenital,Malformation Of Heart,Malformation Of Hearts
D006801	Humans	Members of the species Homo sapiens.	Homo sapiens,Man (Taxonomy),Human,Man, Modern,Modern Man
D013577	Syndrome	A characteristic symptom complex.	Symptom Cluster,Cluster, Symptom,Clusters, Symptom,Symptom Clusters,Syndromes
D014682	Vena Cava, Inferior	The venous trunk which receives blood from the lower extremities and from the pelvic and abdominal organs.	Inferior Vena Cava,Inferior Vena Cavas,Vena Cavas, Inferior
D014683	Vena Cava, Superior	The venous trunk which returns blood from the head, neck, upper extremities and chest.	Superior Vena Cava,Superior Vena Cavas,Vena Cavas, Superior
D014684	Venae Cavae	The inferior and superior venae cavae.	Cavae, Venae