A case of congenital H-type tracheoesophageal fistula was reported. A five-year-old male presented with the symptom of coughing and choking during eating. He had experienced the symptom since the neonatal period. He was frequently admitted with the diagnosis of pneumonia but the definite diagnosis has never been established. The esophagogram revealed communication between cervical esophagus and trachea. The operation was performed by division and suture of the fistula uneventfully. Postoperatively, he could take meals normally. The literature of this condition was also reviewed.