OBJECTIVE To describe an unusual case of congenital fibroepithelial polyp of the prostatic urethra in an adult, presented with acute urinary retention. METHODS Cystouretrographic, endoscopical and pathological investigations are discussed. RESULTS The definitive diagnosis of the tenth case of this benign lesion was made only after endoscopic resection and pathological examination. The complete resolution of the symptoms has been quick. CONCLUSIONS We stress this unusual pathology in order to focus its peculiarity in aetiopathogenesis, diagnosis and treatment.