| D054853 |
Malignant Atrophic Papulosis |
Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown. |
Degos Disease,Kohlmeier-Degos Disease,Degos Syndrome,Degos's Malignant Atrophic Papulosis,Erythrokeratoderma en cocardes,Papulosis, Malignant Atrophic,Atrophic Papuloses, Malignant,Atrophic Papulosis, Malignant,Disease, Degos,Disease, Kohlmeier-Degos,Malignant Atrophic Papuloses,Papuloses, Malignant Atrophic,Syndrome, Degos |
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